Getting Orfadin (Nitisinone) Covered by Cigna in New York: Coding, Appeals & Prior Authorization Guide
Answer Box: Getting Orfadin (Nitisinone) Covered by Cigna in New York
Orfadin (nitisinone) for hereditary tyrosinemia type 1 requires Cigna prior authorization using ICD-10 code E70.29 and HCPCS J8499. Key steps: 1) Confirm HT-1 diagnosis with elevated succinylacetone levels, 2) Submit PA with specialist documentation and dietary management plan,